ANCA-associated glomerulonephrites (GNs) is a group of diseases with damage to the kidney glomeruli with underlying necrotizing vasculitis associated with the formation of antibodies to the cytoplasm of neutrophils. The clinical feature of ANCA-GN is the tendency to a rapidly progressive course of GN with a decrease in glomerular filtration rate of more than by 50% over several weeks or months. The article presents a review of the literature on epidemiology, classification, etiology and pathophysiology, clinical manifestation and treatment of ANCA-associated rapidly progressive GN.

Keywords: rapidly progressive glomerulonephritis, vasculitis